{"id":8983,"date":"2019-01-24T10:14:44","date_gmt":"2019-01-24T10:14:44","guid":{"rendered":"https:\/\/content.www.institutomaxilofacial.com\/es\/?p=8983"},"modified":"2019-01-24T12:21:26","modified_gmt":"2019-01-24T12:21:26","slug":"que-es-el-sindrome-de-moebius","status":"publish","type":"post","link":"https:\/\/content.www.institutomaxilofacial.com\/es\/2019\/01\/24\/que-es-el-sindrome-de-moebius\/","title":{"rendered":"Qu\u00e9 es el S\u00edndrome de Moebius"},"content":{"rendered":"<div class=\"kk-star-ratings kksr-auto kksr-align-right kksr-valign-top\"\n    data-payload='{&quot;align&quot;:&quot;right&quot;,&quot;id&quot;:&quot;8983&quot;,&quot;slug&quot;:&quot;default&quot;,&quot;valign&quot;:&quot;top&quot;,&quot;ignore&quot;:&quot;&quot;,&quot;reference&quot;:&quot;auto&quot;,&quot;class&quot;:&quot;&quot;,&quot;count&quot;:&quot;5&quot;,&quot;legendonly&quot;:&quot;&quot;,&quot;readonly&quot;:&quot;&quot;,&quot;score&quot;:&quot;4.6&quot;,&quot;starsonly&quot;:&quot;&quot;,&quot;best&quot;:&quot;5&quot;,&quot;gap&quot;:&quot;5&quot;,&quot;greet&quot;:&quot;Rate this post&quot;,&quot;legend&quot;:&quot;4.6\\\/5 - (5 votos)&quot;,&quot;size&quot;:&quot;30&quot;,&quot;title&quot;:&quot;Qu\u00e9 es el S\u00edndrome de Moebius&quot;,&quot;width&quot;:&quot;158.5&quot;,&quot;_legend&quot;:&quot;{score}\\\/{best} - ({count} {votes})&quot;,&quot;font_factor&quot;:&quot;1.25&quot;}'>\n            \n<div class=\"kksr-stars\">\n    \n<div class=\"kksr-stars-inactive\">\n            <div class=\"kksr-star\" data-star=\"1\" style=\"padding-right: 5px\">\n            \n\n<div class=\"kksr-icon\" style=\"width: 30px; height: 30px;\"><\/div>\n        <\/div>\n            <div class=\"kksr-star\" data-star=\"2\" style=\"padding-right: 5px\">\n            \n\n<div class=\"kksr-icon\" style=\"width: 30px; height: 30px;\"><\/div>\n        <\/div>\n            <div class=\"kksr-star\" data-star=\"3\" style=\"padding-right: 5px\">\n            \n\n<div class=\"kksr-icon\" style=\"width: 30px; height: 30px;\"><\/div>\n        <\/div>\n            <div class=\"kksr-star\" data-star=\"4\" style=\"padding-right: 5px\">\n            \n\n<div class=\"kksr-icon\" style=\"width: 30px; height: 30px;\"><\/div>\n        <\/div>\n            <div class=\"kksr-star\" data-star=\"5\" style=\"padding-right: 5px\">\n            \n\n<div class=\"kksr-icon\" style=\"width: 30px; height: 30px;\"><\/div>\n        <\/div>\n    <\/div>\n    \n<div class=\"kksr-stars-active\" style=\"width: 158.5px;\">\n            <div class=\"kksr-star\" style=\"padding-right: 5px\">\n            \n\n<div class=\"kksr-icon\" style=\"width: 30px; height: 30px;\"><\/div>\n        <\/div>\n            <div class=\"kksr-star\" style=\"padding-right: 5px\">\n            \n\n<div class=\"kksr-icon\" style=\"width: 30px; height: 30px;\"><\/div>\n        <\/div>\n            <div class=\"kksr-star\" style=\"padding-right: 5px\">\n            \n\n<div class=\"kksr-icon\" style=\"width: 30px; height: 30px;\"><\/div>\n        <\/div>\n            <div class=\"kksr-star\" style=\"padding-right: 5px\">\n            \n\n<div class=\"kksr-icon\" style=\"width: 30px; height: 30px;\"><\/div>\n        <\/div>\n            <div class=\"kksr-star\" style=\"padding-right: 5px\">\n            \n\n<div class=\"kksr-icon\" style=\"width: 30px; height: 30px;\"><\/div>\n        <\/div>\n    <\/div>\n<\/div>\n                \n\n<div class=\"kksr-legend\" style=\"font-size: 24px;\">\n            4.6\/5 - (5 votos)    <\/div>\n    <\/div>\n<p>El <a href=\"http:\/\/www.moebius.org\"><strong>S\u00edndrome de Moebius<\/strong><\/a> es una enfermedad cong\u00e9nita considerada rara (con 1 de cada 120.000 nacidos vivos en nuestro pa\u00eds) cuyas manifestaciones m\u00e1s visibles son la \u201ccara de m\u00e1scara\u201d, es decir, <strong>un rostro inexpresivo<\/strong> debido a la par\u00e1lisis de los nervios que dan movimiento a la musculatura que controla la m\u00edmica y la expresi\u00f3n (frente, cejas, p\u00e1rpados, labios&#8230;), y la<strong> falta de parpadeo y movilidad ocular<\/strong> lateral .<\/p>\n<p>El diagn\u00f3stico del <strong>S\u00edndrome de Moebius<\/strong> suele hacerse en el momento del nacimiento, ya que el reci\u00e9n nacido presenta una cara inexpresiva. En cuanto a sus causas, aunque sigue siendo un \u00e1rea bastante desconocida, existen estudios que apuntan a accidentes vasculares del embri\u00f3n durante el primer trimestre del embarazo (ligados a drogas vasoactivas, hipertermia, traumatismos maternos, etc.) y tambi\u00e9n se ha detectado un componente gen\u00e9tico en aproximadamente un tercio de los casos estudiados. No obstante, <strong>la causa exacta de esta enfermedad sigue siendo desconocida<\/strong> y la literatura medica presenta teor\u00edas que est\u00e1n en conflicto.<\/p>\n<p>El <strong>tratamiento<\/strong> de esta enfermedad es fundamentalmente quir\u00fargico, mediante <strong>dos tipos de cirug\u00eda:<\/strong> por un lado, las de<strong> reanimaci\u00f3n facial activa<\/strong>, que pretenden dar movilidad y expresividad facial (Mioplastia de elongaci\u00f3n de m\u00fasculo temporal seg\u00fan t\u00e9cnica de Labb\u00e9, trasplante de un m\u00fasculo del muslo a la cara&#8230;). Por otro lado, est\u00e1n las <strong>t\u00e9cnicas que mejoran la est\u00e1tica facial<\/strong> (colgajos de fascia, hilos tensores, etc). Estos procedimientos son adem\u00e1s acompa\u00f1ados por <strong>terapias no quir\u00fargicas<\/strong>, como el uso de l\u00e1grimas artificiales, estimulaci\u00f3n facial, sello ocular nocturno, etc.<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\" wp-image-8986 alignleft\" src=\"https:\/\/content.www.institutomaxilofacial.com\/wp-content\/uploads\/2019\/01\/marta-530x617.png\" alt=\"\" width=\"295\" height=\"343\" srcset=\"https:\/\/content.www.institutomaxilofacial.com\/wp-content\/uploads\/2019\/01\/marta-530x617.png 530w, https:\/\/content.www.institutomaxilofacial.com\/wp-content\/uploads\/2019\/01\/marta-1125x1310.png 1125w, https:\/\/content.www.institutomaxilofacial.com\/wp-content\/uploads\/2019\/01\/marta-172x200.png 172w, https:\/\/content.www.institutomaxilofacial.com\/wp-content\/uploads\/2019\/01\/marta-107x125.png 107w, https:\/\/content.www.institutomaxilofacial.com\/wp-content\/uploads\/2019\/01\/marta.png 1171w\" sizes=\"auto, (max-width: 295px) 100vw, 295px\" \/>Aunque el <strong>S\u00edndrome de Moebius<\/strong> suele estar acompa\u00f1ada por otros problemas f\u00edsicos, como malformaciones en pies y manos, estrabismo, o paladar hendido, los afectados no muestran ning\u00fan d\u00e9ficit en materia intelectual.<\/p>\n<p>En <strong>Instituto Maxilofacial<\/strong> hemos tenido la oportunidad de tratar a Marta, una paciente con s\u00edndrome de Moebius, cuyo tratamiento ha consistido principalmente en una<a href=\"https:\/\/content.www.institutomaxilofacial.com\/es\/cirugia-ortognatica\/que-es-la-cirugia-ortognatica\/\"><strong> cirug\u00eda ortogn\u00e1tica<\/strong> <\/a>para corregir su maloclusi\u00f3n y armonizar su esqueleto facial, una <strong>mioplastia de alargamiento<\/strong> del m\u00fasculo temporal, para mejorar la movilidad de las comisuras labiales y darle capacidad de sonrisa, y finalmente<strong> injertos<\/strong> de fascia lata (m\u00fasculo de muslo) para suspender el labio inferior, adem\u00e1s de sesiones terape\u00faticas de <strong>logopedia<\/strong>.<\/p>","protected":false},"excerpt":{"rendered":"<p>El S\u00edndrome de Moebius es una enfermedad cong\u00e9nita considerada rara (con 1 de cada 120.000 nacidos vivos en nuestro pa\u00eds) cuyas manifestaciones m\u00e1s visibles son la \u201ccara de m\u00e1scara\u201d, es decir, un rostro inexpresivo debido a la par\u00e1lisis de los nervios que dan movimiento a &#8230;<\/p>\n","protected":false},"author":6,"featured_media":8984,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[374,53],"tags":[147,55,134,275],"class_list":["post-8983","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-cirugia-estetica-maxilofacial","category-cirugia-ortognatica-estetica-facial","tag-centro-medico-teknon","tag-cirugia-maxilofacial","tag-cirugia-minimamente-invasiva","tag-dra-adaia-valls"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.2 - 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